Skip to main content

Table 1 Forms of Angioedemas without wheals

From: Idiopathic non-histaminergic acquired angioedema: a case series and discussion of published clinical trials

Hereditary angioedemas

HAE with C1-inhibitor deficiency (C1-INH_HAE)

HAE with FXII mutations (FXII-HAE)

HAE of unknown origin (U-HAE)

Acquired angioedemas

Idiopathic histaminergic acquired angioedema (IH-AAE)

Idiopathic non-histaminergic acuired angioedema (InH-AAE)

Acquired angioedema related to angiotensin-converting enzyme inhibitor (ACEi-AAE)

Aquired angioedema with C1-inhibitor deficiency (C1-INH-AAE)

  1. Modified from Cicardi et al. [4]