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Table 4 Hematological malignancies in patients with Schnitzler’s syndrome

From: Schnitzler’s syndrome: lessons from 281 cases

Malignancies

Cases

Years after onset SchS

Waldenström’s macroglobulinemia

21

1-23, median 8

Lymphoplasmacytic lymphoma, other

3

3,7,?

Non-Hodgkin lymphoplasmocytic mantellar lymphoma

1

?

Non-Hodgkin lymphoma, not specified

2

?

Splenic marginal zone lymphoma

1

8

Marginal zone B-cell lymphoma

1

7

B-cell lymphoma, not specified

2

?,?

Multiple myeloma

2

2,13

Chronic lymphocytic leukemia

1

10

Acute myeloid leukemia

1

?

Total

35

median 8 years